ArcPathVisio
Brace
Octagon
Ellipse
EndoplasmicReticulum
HexagonPathVisio
GolgiApparatus
MimDegradation
Mitochondria
Octagon
PentagonPathVisio
Rectangle
RoundedRectangle
SarcoplasmicReticulum
TrianglePathVisio
none
Apical surface
of renal tubule
Dicarboxylic
amino aciduria (DA)
Basolateral surface
of renal tubule
Basic AA
Arginine
Lysine
Histidine
Neutral AA
Alanine
Na+
Asparagine
Cysteine
Glutamine
Glycine
Isoleucine
Leucine
Methionine
Phenylalanine
Proline
Serine
Threonine
Tryptophan
Tyrosine
Valine
L-cysteine
3 Na+
Cystine
K+
SLC7A7
SLC1A1
L-glutamate
L-aspartate
D-aspartate
Acidic AA
H+
SLC36A2
SLC6A20
SLC6A19
TMEM27
SLC3A1
SLC7A9
3 Na+
K+
H+
L-glutamate
L-aspartate
D-aspartate
Acidic AA
L-cysteine
H+
Glycine
Imino AA
Proline
H+
Glycine
Imino AA
Proline
Proline
Cl-
2 Na+
Proline
Cl-
2 Na+
Iminoglycinuria
Neutral AA
Alanine
Na+
Asparagine
Cysteine
Glutamine
Glycine
Isoleucine
Leucine
Methionine
Phenylalanine
Proline
Serine
Threonine
Tryptophan
Tyrosine
Valine
Hartnup
disorder (HD)
Cystinuria
Basic AA
Arginine
Lysine
Histidine
Neutral AA
Cystine
Neutral AA
SLC3A2
Neutral AA
Na+
Basic AA
Basic AA
Neutral AA
Na+
Lysinuric protein
intolerance (LPI)
Tubulus lumen
Name: Amino acid transport defects (IEMs)
Last Modified: 20240212045550
Organism: Homo sapiens