Mitochondrial long chain fatty acid beta-oxidation (WP368)

Homo sapiens

Proteins on this pathway have targeted assays available via the [ CPTAC Assay Portal]


Niradiz Reyes , Thomas Kelder , Kristina Hanspers , Jildau Bouwman , Martijn Van Iersel , Alex Pico , Egon Willighagen , Daniela Digles , Zahra Roudbari , Marianthi Kalafati , Martina Summer-Kutmon , Irene Hemel , and Eric Weitz


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Homo sapiens



Pathway Ontology

fatty acid beta degradation pathway fatty acid beta degradation pathway classic metabolic pathway


Label Type Compact URI Comment
Long chain Acyl-CoA Metabolite chebi:83139
3-Ketoacyl-CoA Metabolite chebi:57347
Acetyl-CoA Metabolite cas:72-89-9
Long Chain Fatty Acid Metabolite chebi:15904
trans-D2-Enoyl-CoA Metabolite chebi:10723
Acyl-CoA (n-2) Metabolite chebi:17984
ACSL4 GeneProduct ncbigene:2182
SCP2 GeneProduct ncbigene:6342
CPT2 GeneProduct ncbigene:1376
EHHADH GeneProduct ncbigene:1962
ACSL1 GeneProduct ncbigene:2180
DCI GeneProduct ncbigene:1632
ACADS GeneProduct ncbigene:35
HADHA GeneProduct ncbigene:3030 similiar to: ECHA RAT
CPT1A GeneProduct ncbigene:1374
ACSL2 GeneProduct ncbigene:80221
ACSL3 GeneProduct ncbigene:2181
ACADL GeneProduct ncbigene:33
ACADM GeneProduct ncbigene:34
ACADVL GeneProduct ncbigene:37
HADHSC GeneProduct ncbigene:3033
SLC25A20 GeneProduct ncbigene:788
PECR GeneProduct ncbigene:55825